1 | P a g e ATI PN PEDIATRICS PROCTORED EXAM 4 NEWEST VERSIONS| WITH ACTUAL CORRECT QUESTIONS AND VERIFIED DETAILED RATIONALES ANSWERS| 2024(NEWEST) ALREADY GRADED A+ PKU will causes _______ ______if left untreated Mental Retardation rationale: Phenylketonuria (PKU) is a recessive hereditary defect of metabolism that, if untreated, causes severe mental retardation. It is not related to congenital heart defects, increased intracranial pressure, or to a strangulated intestine. In working with the child or family of a child with a congenital disorder, the most effective nursing intervention for this child or family would be for the nurse to Use reflective listening and offer nonjudgmental support rationale: Families are naturally apprehensive and find it difficult not to overprotect a child who is ill. They often increase the child's anxiety and cause fear in the child about participating in normal activities. Children are rather sensible about finding their own limitations and usually limit their activities to their capacity if they are not made unduly apprehensive. Some families can adjust well and provide guidance and security for the sick child. Others may become confused and frightened and show hostility, disinterest, or neglect; these families need guidance and counseling. The nurse has a