Paea Pediatrics Eor Topics Questions And Answers (Updated )

cystic fibrosis is an autosomal _________ disorder of defective CF transmembrane receptor (CFTR) protein that prevents _________ transport resulting in a buildup of thick, viscous, mucus in what 5+ organs? w/ an increased incidence in what population? {Ans: -autosomal recessive -chloride -lungs, pancreas, liver, intestines, reproductive tracts -inc incidence in caucausians}foreign body aspiration is more commonly going to obstruct the L or R main bronchus? sx's? dx by? {Ans: R- it is wider, more vertical, and shorter than L sx: coughing, choking, wheezing, hemoptysis dx by: CXR & *bronchoscopy* (direct visualization & removal)}patent ductus arteriosus is a communication between what 2 vessels? what can occur if PDA is left untreated? {Ans: -pulmonary artery and descending aorta -Eisenmenger's syndrome: pulmonary HTN resulting from the L to R shunt switching to R to L over time resulting in cyanosis}Dx? a 3 year old comes in with a h/o high fever that lasted 4 days and has broken but now has a rash that is rose/pink colored maculopapular and blanchable that started on the trunk/back and has spread to the face; tx? {Ans: dx: roseola infantum (sixth's disease) caused by human herpes virus 6 or 7 (this is the