NURS 4010 C:APTER 25::EMATOLOGY PRACT=CE TEST VER=F=ED 100% GRADED A+ B. Prevention and treatment of pain The goal of medical management is to prevent pain and promote growth and development. :ydration and prevention of stress and illness will limit sickle cell crisis episodes, but because pain is the first sign of a crisis, plans must be in place to treat pain expediently. Children with sickle cell disease do not require additional oxygen unless in crisis. They do not require supplemental iron. They may receive transfusions during a crisis, but this is not a routine or planned part of their therapy unless they are in crisis. The therapeutic management of children with sickle cell disease consists primarily of which of the following? A.Oxygen therapy B.Prevention and treatment of pain C.Adequate hydration D.Frequent blood transfusions A. Sickle Cell Disease __________: an inherited group of disorders, red blood cells contort into a sickle shape. Partial or complete replacement of normal hemoglobin with abnormal hemoglobin S (:gb S). :emoglobin in the RBCs takes on an elongated "sickle" shape. Sickled cells are rigid and obstruct capillary blood flow. Microscopic obstructions lead to engorgement and tissue ischemia. :ypoxia occurs and causes sickling, leading to pain. A.